Repair of atrial septal defect with Eisenmenger syndrome after long-term sildenafil therapy.
نویسندگان
چکیده
We report a woman with atrial septal defect and severe pulmonary hypertension with 25.0 Wood unit.m(2) of indexed total pulmonary vascular resistance. She underwent successful corrective repair of atrial septal defect after 2 years of treatment with sildenafil, and has been monitored for 4 years after repair. This case supports a "treat and repair" approach using advanced pulmonary vasodilator therapy in selected patients with inoperable severe pulmonary hypertension associated with atrial septal defect.
منابع مشابه
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Eisenmenger Syndrome To the Editor: Michelakis et al1 report encouraging results with the use of sildenafil in patients with pulmonary hypertension. The authors included a patient with repaired congenital heart disease (and a small residual ventricular septal defect) who has pulmonary vascular disease, but also labeled him as having the Eisenmenger syndrome. This is unfortunate, as it gives the...
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ورودعنوان ژورنال:
- The Annals of thoracic surgery
دوره 89 5 شماره
صفحات -
تاریخ انتشار 2010